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Epithelioid sarcoma

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Epithelioid sarcoma (Medical Condition)

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Perivascular epithelioid cell tumour (Medical Condition)

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Advanced High Grade Abdominal Sarcoma | Sarcoma Oncology Center

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MSK Tumor C1 PET CT Osteosarcoma

Epithelioid sarcoma is a rare soft tissue sarcoma arising from mesenchymal tissue and characterized by epithelioid-like features. It accounts for less than 1% of all soft tissue sarcomas. It was first clearly characterized by F.M. Enzinger in 1970. It commonly presents itself in the distal limbs of young adults as a small, soft mass or a series of bumps. A proximal version has also been described, frequently occurring in the upper extremities. Rare cases have been reported in the pelvis, vulva, penis, and spine.